Pediatr Transplant 2020 Jan 27
Improvement of native pulmonary alveolar proteinosis after contralateral single living-donor lobar lung transplantation: A case report.
Kobayashi K, Ohkouchi S, Sasahara Y, Ebina M, Nakata K, Saito R, Akiba M, Sado T, Oishi H, Watanabe T, Kurosawa H, Okada Y
PAP is a rare disease characterized by the accumulation of surfactant materials in the alveolar spaces due to the imbalance of surfactant homeostasis ...
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Source: PubMed
J. Clin. Invest. 2020 Jan 21
Steroid-resistance in Diamond Blackfan anemia associates with p57Kip2 dysregulation in erythroid progenitors.
Ashley RJ, Yan H, Wang N, Hale J, Dulmovits BM, Papoin J, Olive ME, Udeshi ND, Carr SA, Vlachos A, Lipton JM, Da Costa L, Hillyer CD, Kinet S, Taylor N, Mohandas N, Narla A, Blanc L
Despite the effective clinical use of steroids for the treatment of Diamond Blackfan anemia (DBA), the mechanistic bases via which glucocorticoids reg ...
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Source: PubMed
Drug Discov Ther
Gene disruption of ribosomal protein L5 (RPL5) decreased the sensitivity of CHO-K1 cells to uncoupler carbonylcyanide-3-chlorophenylhydrazone.
Araki M, Ishibashi T, Munesue M, Ohashi K, Nobukuni Y, Maeda M
Protonophoric uncoupler carbonylcyanide-3-chlorophenylhydrazone (CCCP) decreases the proton motive force (?P) of the mitochondrial inner membrane and ...
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Source: PubMed
Turk. J. Pediatr.
Outcome of allogeneic Hematopoietic Stem Cell Transplantation on Diamond-Blackfan anemia using busulfan-based myeloablative regimen.
Behfar M, Koochakzadeh L, Yazdanian N, Salajegheh P, Rostami T, Khodayari-Namini N, Ghavamzadeh A, Hamidieh AA
Behfar M, Koochakzadeh L, Yazdanian N, Salajegheh P, Rostami T, Khodayari-Namini N, Ghavamzadeh A, Hamidieh AA. Outcome of allogeneic Hematopoietic St ...
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Source: PubMed
RNA 2020 Jan 07
Hypoxia influences polysome distribution of human ribosomal protein S12 and alternative splicing of ribosomal protein mRNAs.
Brumwell A, Fell L, Obress L, Uniacke J
Ribosomes were once considered static in their composition because of their essential role in protein synthesis and kingdom-wide conservation. The exi ...
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Source: PubMed
