Cruveilhier-baumgarten Syndrome

Other Names :  

Pégot-Cruveilhier–Baumgarten disease, Baumgarten’s portal hypertension variant syndrome, Baumgarten’s syndrome, Cruveilhier - Baumgarten cirrhosis, Cruveilhier-Baumgarten sound

What is Cruveilhier-baumgarten Syndrome ?  

It is a rare medical condition with distension of umbilical or paraumbilical veins, characterized by the presence of an abdominal wall bruit and a palpable thrill. There is portal hypertension, splenomegaly, hypersplenism and esophageal varices.Liver may be smaller than normal.


Cause(s) :  

• The blood flowing through paraumbilical vein bypasses the liver, causing the condition.

Symptoms :  

• Liver cirrhosis, small size of liver
• Enlarged spleen
• Patent Umbilical veins
• Portal hypertension

Specialist to consult :  Hepatology

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