Creutzfeldt-Jakob Disease (CJD) is a rare disease caused by mutations in a person’s brain. It is not contagious and may affect one in every one million people.
A 63-year-old Australian has been diagnosed with a rare degenerative brain disease. Health authorities stressed that the condition was unrelated to mad cow disease and not contagious. The man, named by the media as Frank Burton, is in a serious condition in hospital with a likely case of "classical Creutzfeldt-Jakob Disease (CJD)", said a spokesman for Sydney Local Health District.
Burton, a former chief financial officer for Aussie Rules football team Sydney Swans was told he had three months to live but this has now been reduced to two or three weeks, his friend Peter Kogoy said.
"(He has gone) from having a head of dark, straight (hair) and black beard, to totally white, totally white," Kogoy told the Australian Broadcasting Corporation.
"A total loss of speech and total loss of movement in his limbs in a matter of weeks and days."
"Variant CJD" emerged in Britain in the late 1980s and 1990s and was linked to mad cow disease, officially known as bovine spongiform encephalopathy (BSE), which causes a brain-destroying disorder in humans.
But the Sydney health district said "classical CJD" was not linked to mad cow and there have been no cases of BSE in Australia.
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"Classical CJD is an extremely rare disease. The chance of someone in the community having the disease is around one in every one million people," the health district said in a statement.
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The causes of death are usually infection, heart failure, or respiratory failure.
Source-AFP